Osteogenesis Imperfecta Treatment

Osteogenesis imperfecta is a congenital disease, there is no special treatment. The main Osteogenesis imperfecta treatment is to prevent fractures and improve the load power line, to increase bone strength, improve bone marrow function, the protection of the infant.

Treatment of osteogenesis imperfecta associated with pain symptoms in patients with osteogenesis imperfecta, joint use of rocaltrol capsule and Miacalcic, medication to alleviate symptoms after a few weeks, 3 months after the increase in bone mineral density, cortical bone thickening.

With the development of rehabilitation medicine, Gerber for babies and children of patients with osteogenesis imperfecta, the concept of rehabilitation. Strict protection in the water treatment, upright exercises to strengthen the pelvic and lower limb muscle strength. Upright independent after the long legs standing practice stationery under the protection of future protective support, the help of walking exercise walking device. General together with the surgical treatment of patients can receive better results. Letts children and so on can wear trousers vacuum orthosis standing practice, this method comfortable, safe and can reduce the incidence of fractures. Rehabilitation treatment, bone mineral density also increased.

For a fixed fracture, increasing the strength of bone fragility, infancy, or by using percutaneous pinning intramedullary fracture treatment, the time being to maintain bone strength line-line, pinning the requirements at this time may not be entirely through the medullary cavity, some myeloid cavity, some bone at the side, but also assist, 3-to 4-year-old after the replacement of the intramedullary extension of the sting. A number of cut-off in bone marrow may be an extension of intramedullary nail or strut orthopedic surgery is the treatment of osteogenesis imperfecta due to a malformation complex effective way. Can correct a number of deformities, bone reasonable rearrange-line, to strengthen the fragile bone strength, significant improvement in function. Choose the operation should not be very serious cases, should be selected after the limb deformity correction, there is the restoration of standing, walking cases. Right to determine the estimate of the actual status of bone deformity is very important not only as the backbone of deformity angle, bending bow, often have a serious reverse, in general on x-ray film, it is difficult to determine the width of the medullary cavity, multi-segment osteotomy, the expansion of medullary cavity . After the reorganization, in which the supportive structures strengthened, must be fully pre-operative preparation. Intramedullary strut can be extended, there are two types: Balley-hoon bow under par and Sheffield. Structures placed within the length must be enough. Such as femur, distal want through the ceiling, direct inter-stamp equal to the location of adults, and the arrow on the side of the central or near central location, only the backbone and the metaphysis of the best to play a supporting role within. Bilateral femoral and tibial deformities, correction should be graded first bilateral femur, and tibia to correct bilateral. At the same time, the ipsilateral femur and tibia to correct bone deformities, after very difficult to maintain. Do not need the general femur bone, the tibia of age many children the best bone graft osteotomy paragraph, because there is that there is no possible healing. Proximal femoral osteotomy line is too high, there is likely to occur after hip varus. Bone healing after a long time, reliable support with adequate protection is essential. With the growth in children with a view to the optional replacement of structures within.

50% 1 70% of osteogenesis imperfecta associated with spinal deformities that can be used to protect stent. If more than 60 ° scoliosis, the treatment is very difficult, lightweight materials stationery does not work, can also seriously consider spinal fusion. Older women on estrogen can be used to reduce the severe osteoporosis.